第一临床医学院知识库

目的：提高临床医师对小儿炎性肌纤维母细胞瘤（inflammatory myofibroblastic tumor,IMT）的临床特点、诊断及治疗的认识，以及明确其诊治方法。方法：报告2例小儿炎性肌纤维母细胞瘤的临床表现、实验室检查、影像学检查、诊治方法及相关文献复习。

结果：2例均经手术治疗完整切除肿瘤，术后恢复良好，随访1年到3年均无复发。结论：IMT是一种罕见的软组织肿瘤，可以发生在人体的任何软组织部位及任何年龄，但通常出现在儿童及年轻的（<40岁）成人。其诊断的金标准是病理学及免疫组织化学分析，手术切除是最有效和最根本的治疗,大部分病例预后良好。

Objetive:To improve the recognization in clinical manifestations,diagnosis,and treatment of pediatric inflammatory myofibroblastic tumors,and to clear diagnosis and treatment of IMT. Methods:Report clinical manifestations, laboratorial examinations,imagings,diagnosis and treatment methods of pediatric inflammatory myofibroblastic tumors in two cases and review the literature about IMT. 

Results:A complete resection in 2 cases through surgical treatment,having a good recovery and no one recurrence after being followed up about one year to three years. Conclusions:IMT is a rare soft-tissue tumor,it can occur at any site in the body and at any age,but commonly being seen in children and young adults(<40 years old).Pathol-ogical and immunocytochemical analyses are the "gold standards" for the diagnosis of IMTs. Surgical resection is the most effective and radical treatment.Also,IMT has a good prognosis.